Persistent Mullerian duct syndrome with transverse testicular ectopia: rare presentation of inguinal hernia.

نویسندگان

  • Ashish Gupta
  • Nilanjan Panda
  • Makhan Lal Saha
  • Shuvro Ganguly
  • Samik Kumar Bandyopadhyay
  • Ruchira Das
چکیده

INTRODUCTION Persistent Mullerian duct syndrome (PMDS) is a rare type of pseudohermaphroditism in genotypically and phenotypically males. They have a uterus, fallopian tubes, and upper part of the vagina; but Mullerian duct fails to regress. In transverse testicular ectopia (TTE), one of the testis moves to the opposite side and both testes pass the same inguinal canal. We report a case of PMDS with TTE presented with a left-sided inguinal hernia and right undescended testis.

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Persistent Mullerian duct syndrome with transverse testicular ectopia presenting in an irreducible recurrent inguinal hernia.

Persistent Mullerian duct syndrome (PMDS), a form of male pseudohermaphroditism, is rare. This is a case report of 40-years-old, an otherwise normal male, presenting with Mullerian duct derivatives and transverse testicular ectopia (TTE) in the sac of irreducible recurrent inguinal hernia.

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Received January 2008 Accepted October 2008 INTRODUCTION Persistent mullerian duct syndrome (PMDS), or hernia uteri inguinale, describes a group of patients with a 46,XY karyotype and normal male external genitalia, but internal mullerian duct structures. Typically, these phenotypic males have unilateral or bilateral undescended testes, bilateral fallopian tubes, a uterus, and an upper vaginal ...

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عنوان ژورنال:
  • Urology journal

دوره 10 2  شماره 

صفحات  -

تاریخ انتشار 2013