Persistent Mullerian duct syndrome with transverse testicular ectopia: rare presentation of inguinal hernia.
نویسندگان
چکیده
INTRODUCTION Persistent Mullerian duct syndrome (PMDS) is a rare type of pseudohermaphroditism in genotypically and phenotypically males. They have a uterus, fallopian tubes, and upper part of the vagina; but Mullerian duct fails to regress. In transverse testicular ectopia (TTE), one of the testis moves to the opposite side and both testes pass the same inguinal canal. We report a case of PMDS with TTE presented with a left-sided inguinal hernia and right undescended testis.
منابع مشابه
Persistent Mullerian duct syndrome with transverse testicular ectopia presenting in an irreducible recurrent inguinal hernia.
Persistent Mullerian duct syndrome (PMDS), a form of male pseudohermaphroditism, is rare. This is a case report of 40-years-old, an otherwise normal male, presenting with Mullerian duct derivatives and transverse testicular ectopia (TTE) in the sac of irreducible recurrent inguinal hernia.
متن کاملTransverse Testicular Ectopia: A Rare Presentation with Persistent Müllerian Duct Syndrome
Undescended testes can be found in the inguinal channel or in the abdomen. Rarely, undescended testes can present with transverse testicular ectopia (TTE) and very rarely, with residual Müllerian duct (MD) structures. This latter presentation is called persistent MD syndrome (PMDS). PMDS is mostly discovered during surgery for inguinal hernia or cryptorchidism. TTE is a rare congenital anomaly ...
متن کاملCombined persistent Mullerian Duct Syndrome, Transverse Testicular Ectopia and Mosaic Klinefelter's Syndrome.
Persistent Mullerian Duct Syndrome (PMDS), a rare form of male pseudohermaphroditism, is characterized by the persistence of Mullerian duct structures (uterus, fallopian tubes and upper two-thirds of vagina) in otherwise normallyvirilized males (Karyotype 46XY). Patients suffering from PMDS present with cryptorchidism, inguinal hernia and infertility. Diagnosis is established when Mullerian duc...
متن کاملPersistent mullerian duct syndrome with an irreducible inguinal hernia.
Received January 2008 Accepted October 2008 INTRODUCTION Persistent mullerian duct syndrome (PMDS), or hernia uteri inguinale, describes a group of patients with a 46,XY karyotype and normal male external genitalia, but internal mullerian duct structures. Typically, these phenotypic males have unilateral or bilateral undescended testes, bilateral fallopian tubes, a uterus, and an upper vaginal ...
متن کاملTransverse testicular ectopia, a case report and review of literature
Crossed testicular ectopia (CTE)/transverse testicular ectopia (TTE) is a rare but well known congenital anomaly, in which both gonads migrate toward the same hemiscrotum. It is usually associated with other abnormalities such as persistent Mullerian duct syndrome, true hermaphroditism, inguinal hernia, hypospadias, pseudohermaphroditism, and scrotal anomalies. About 100 cases of transverse tes...
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ورودعنوان ژورنال:
- Urology journal
دوره 10 2 شماره
صفحات -
تاریخ انتشار 2013